Classical Systemic Autoimmune Diseases -- Systemic Lupus Erythematosus -- Antiphospholipid Syndrome -- Rheumatoid Arthritis -- Macrophage Activation Syndrome in Juvenile Idiopathic Arthritis -- Adult Still Disease -- Systemic Sclerosis -- Sjögren Syndrome -- Mixed Connective Tissue Disease -- Relapsing Polychondritis -- Raynaud Phenomenon -- Drug-Induced Autoimmunity -- The Multiple Autoimmune Syndromes -- Systemic Vasculitis -- Giant Cell Arteritis -- Polymyalgia Rheumatica -- Takayasu Arteritis -- Polyarteritis Nodosa -- Microscopic Polyangiitis -- Wegener Granulomatosis -- Churg-Strauss Syndrome -- Buerger Disease -- Behçet Disease -- Susac Syndrome -- Goodpasture Disease -- Kawasaki Disease -- Cogan Syndrome -- Henoch-Shoenlein Purpura -- Cryoglobulinemic Syndrome -- Hypersensitivity Angiitis -- Idiopathic Inflammatory Myopathies -- Polymyositis -- Dermatomyositis -- Clinically Amyopathic Dermatomyositis -- Sporadic Inclusion Body Myositis -- Antisynthetase Syndrome -- Granulomatous Myositis -- Eosinophilic Myositis -- Eosinophilic Fasciitis -- Other Immune-Mediated Systemic Diseases -- Sarcoidosis -- Spondyloarthropathies -- Periodic Fever Syndromes -- Fibromyalgia Syndrome -- Endocrine and Reproductive Autoimmune Diseases -- Hashimoto Thyroiditis -- Atrophic Thyroiditis -- Subacute Thyroiditis -- Graves Disease -- Postpartum Thyroiditis -- Autoimmune Diabetes Mellitus -- Autoimmune Addison Disease or Autoimmune Adrenalitis -- Autoimmune Hypophysitis -- Autoimmune Parathyroid Disease -- Autoimmune Polyendocrine Syndromes -- Endometriosis -- Autoimmune Ovarian Failure -- Autoimmune Orchitis -- Hepatobiliary and Pancreatic Autoimmune Diseases -- Autoimmune Hepatitis -- Primary Biliary Cirrhosis -- Primary Sclerosing Cholangitis -- Extrahepatic Manifestations in Patients with Chronic Hepatitis C Virus Infection -- Autoimmune Pancreatitis -- Gastrointestinal Autoimmune Diseases -- Autoimmune Gastritis -- Ulcerative Colitis -- Inflammatory Bowel Disease -- Celiac Disease -- Cutaneous Autoimmune Diseases -- Cutaneous Lupus Erythematosus -- Pemphigus and Bullous Pemphigoid -- Vitiligo -- Psoriatic Arthropathy -- Cardiovascular and Pulmonary Autoimmune Diseases -- Autoimmune Dilated Cardiomyopathy -- Are Autoimmune Manifestations in Human Dilated Cardiomyopathy Primary or Secondary Events? -- Rheumatic Fever -- Accelerated Atherosclerosis in Autoimmune Diseases -- Idiopathic Interstitial Pneumonias -- Pulmonary Arterial Hypertension -- Neurological Autoimmune Diseases -- Multiple Sclerosis -- Myasthenia Gravis -- Lambert-Eaton Myasthenic Syndrome -- Amyotrophic Lateral Sclerosis -- Paraneoplastic Neurological Syndromes -- Guillain-Barré and Other Immune-Mediated Neuropathies -- Neuromylelitis Optica (Devic Syndrome) -- Central Nervous System Vasculitis -- Autoimmune Epilepsy -- Autoimmune Chorea -- Autoimmune Sensorineural Hearing Loss -- Ocular Autoimmune Diseases -- Autoimmune Retinopathies -- Autoimmune Uveitis -- Vogt-Koyanagi-Harada Disease -- Orbital Myositis -- Renal Autoimmune Diseases -- IgA Nephropathy -- Membranous Nephropathy -- Minimal Change Nephropathy -- Focal and Segmental Glomerulosclerosis -- Membranoproliferative or Mesangiocapillary Glomulonephritis -- Hematologic Autoimmune Diseases -- Autoimmune Hemolytic Anemia -- Pernicious Anemia -- Idiopathic Aplastic Anemia -- Acquired Adult Pure Red Cell Aplasia -- Myelodysplastic Syndromes -- Autoimmune Lymphopenia -- Autoimmune Neutropenia -- Autoimmune Thrombocytopenic Purpura -- Thrombotic Thrombocytopenic Purpura and Other Thrombotic Microangiopathic Hemolytic Anemias -- Heparin-Induced Thrombocytopenia -- Autoimmune Coagulopathies. According to the Autoimmune Diseases Coordinating Committee (ADCC), between 14.7 and 23.5 million people in the USA-up to eight percent of the population-are affected by autoimmune disease. Autoimmune diseases are a family of more than 100 chronic, and often disabling, illnesses that develop when underlying defects in the immune system lead the body to attack its own organs, tissues, and cells. In Diagnostic Criteria in Autoimmune Disease, the editors have gathered in a comprehensive handbook a critical review, by renowned experts, of more than 100 autoimmune diseases, divided into two main groups, namely systemic and organ-specific autoimmune diseases. A contemporary overview of these conditions with special emphasis on diagnosis is presented. Each chapter contains the essential information required by attending physicians as well as bench scientists to understand the definition of a specific autoimmune disease, the diagnostic criteria, and the treatment.